Аннотация
Бемории Гиршпрунг бемории модарзодӣ буда, дар натиҷаи вайроншавии инкишофи системаи асаби энтерикӣ ва набудани ҳуҷайраҳои ганглионӣ дар қисми осебдидаи рӯда ба вуҷуд меояд. Мақсади баррасӣ ҷамъбаст намудани маълумоти муосир оид ба этиология, патогенез, тасниф, зуҳуроти клиникӣ, ташхис ва табобати ҷарроҳии беморӣ мебошад.
Ҷустуҷӯи адабиёт дар пойгоҳҳои PubMed, Scopus, Web of Science ва eLibrary гузаронида шуд. Масъалаҳои ташхис, аз ҷумла биопсияи ректалӣ, усулҳои ҷарроҳии Swenson, Duhamel ва Soave, оризаҳои баъдиҷарроҳӣ ва зарурати назорати дарозмуддат баррасӣ шудаанд. Муносибати муосир интихоби инфиродии тактикаи ҷарроҳӣ ва назорати дарозмуддатро талаб мекунад.
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Феҳристи манбаъ
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